ARTICLES THROMBOSIS & HAEMOSTASIS

Plasma ADAMTS13 activity and von Willebrand factor antigen and activity
in patients with subarachnoid haemorrhage
Kumar, W. Cao, J. K. McDaniel, H. P. Pham, D. Raju, K. Nawalinski, S. Frangos,

D. Kung, E. Zager, S. E. Kasner, J. M. Levine, X. L. Zheng

Long-term safety and efficacy of extended-interval prophylaxis with recombinant
factor IX Fc fusion protein (rFIXFc) in subjects with haemophilia B
J. Pasi, K. Fischer, M. Ragni, B. Nolan, D. J. Perry, R. Kulkarni, M. Ozelo, J. Mahlangu,

A. D. Shapiro, R. I. Baker, C. M. Bennett, C. Barnes, J. Oldenburg, T. Matsushita, H. Yuan,
A. Ramirez-Santiago, G. F. Pierce, G. Allen, B. Mei

Clinical evaluation of glycoPEGylated recombinant FVIII: Efficacy and safety in
severe haemophilia A
P. Giangrande, T. Andreeva, P. Chowdary, S. Ehrenforth, H. Hanabusa, F. W. G. Leebeek,

S. R. Lentz, L. Nemes, L. H. Poulsen, E. Santagostino, C. W. You, W. H. O. Clausen,
P. G. Jönsson, J. Oldenburg, for the Pathfinder™2 Investigators

ADAMTS13 deficiency promotes microthrombosis in a murine model of
diet-induced liver steatosis
Geys, D. Bauters, E. Roose, C. Tersteeg, K. Vanhoorelbeke, M. F. Hoylaerts,

R. H. Lijnen, I. Scroyen

Monitoring of coagulation factor therapy in patients with von Willebrand
disease type 3 using a microchip flow chamber system
Ågren, M. Holmström, D. E. Schmidt, K. Hosokawa, M. Blombäck, P. Hjemdahl

A novel platelet-type von Willebrand disease mutation (GP1BA p.Met255Ile)
associated with type 2B “Malmö/New York” von Willebrand disease
Lavenu-Bombled, C. Guitton, A. Dupuis, M.-J. Baas, C. Desconclois, M. Dreyfus, R. Li,

C. Caron, C. Gachet, E. Fressinaud, F. Lanza

Recommendation for ISTH/SSC Criterion 2015 for autoimmune
acquired factor XIII/13 deficiency
A. Ichinose, H. P. Kohler, H. Philippou, on behalf of the Factor XIII and Fibrinogen

SSC Subcommittee of the ISTH

The D173G mutation in ADAMTS-13 causes a severe form of
congenital thrombotic thrombocytopenic purpura
A clinical, biochemical and in silico study
S. Lancellotti, F. Peyvandi, M. Pagliari, A. Cairo, S. Abdel-Azeim, E. Chermak,

I. Lazzareschi, S. Mastrangelo, L. Cavallo, R. Oliva, R. De Cristofaro

Carboxiterminal pro-endothelin-1 as an endothelial cell biomarker
in thrombotic thrombocytopenic purpura
B. Mikes, G. Sinkovits, P. Farkas, D. Csuka, K. Rázsó, M. Réti, G. Radványi,

J. Demeter, Z. Prohászka

Long-acting recombinant factor VIII Fc fusion protein (rFVIIIFc)
for perioperative haemostatic management in severe haemophilia A
N. Mahlangu, M. Ragni, N. Gupta, S. Rangarajan, R. Klamroth, J. Oldenburg,

K. Nogami, G. Young, L. M. Cristiano, Y. Dong, G. Allen, G. F. Pierce, B. Robinson